2A84.0

ICD-11 MMS 2026-01

Alpha heavy chain disease

Description

The small intestinal morphologic changes are consistent with a mucosa-associated lymphoid tissue lymphoma (MALT lymphoma).

Index terms

  • Alpha heavy chain disease
  • alpha heavy chain disease without mention of remission
  • Alpha heavy chain disease in complete remission
Show allHide
  • Immunoproliferative small intestinal disease
  • IPSID - [Immunoproliferative small intestinal disease]
  • Immunoproliferative small intestinal disease without mention of remission
  • Immunoproliferative small intestinal disease, in complete remission

Exclusions from above levels

  • 2E03 – Malignant neoplasm metastasis in bone or bone marrow
  • http://id.who.int/icd/entity/501778925 – Malignant neoplasm metastasis in lymph nodes
  • http://id.who.int/icd/entity/97145147 – Malignant neoplasm metastasis in thymus gland

Sibling codes

  • 2A84.1 – Gamma heavy chain disease
  • 2A84.2 – Mu heavy chain disease
  • 2A84.Y – Other specified malignant immunoproliferative diseases
  • 2A84.Z – Heavy chain diseases, unspecified

Foundation entity

Alpha heavy chain disease – http://id.who.int/icd/entity/680227490

Allowed postcoordination axes

Part of: 2A84: Heavy chain diseases or malignant immunoproliferative diseases › 02: Neoplasms