3A20.5

ICD-11 MMS 2026-01

Evans syndrome

Description

Evans syndrome is characterised by the association of autoimmune haemolytic anaemia with another haematological anomaly. The thrombocytopaenia may precede, occur concurrently with, or secondary to the autoimmune haemolytic anaemia.

Index terms

  • Evans syndrome

Exclusions from above levels

  • 04 – Diseases of the immune system
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth or the puerperium
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  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations or chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes
  • http://id.who.int/icd/entity/1000704511 – Human immunodeficiency virus disease
  • JB64.1 – Other diseases of the blood or blood-forming organs or certain disorders involving the immune mechanism complicating pregnancy, childbirth or the puerperium

Sibling codes

  • 3A20.0 – Autoimmune haemolytic anaemia, warm type
  • 3A20.1 – Autoimmune haemolytic anaemia, cold type
  • 3A20.2 – Autoimmune haemolytic anaemia, mixed type, cold and warm
  • 3A20.3 – Paroxysmal cold haemoglobinuria
  • 3A20.4 – Alloimmune haemolytic anaemia
  • 3A20.Y – Other specified acquired haemolytic anaemia, immune
  • 3A20.Z – Acquired haemolytic anaemia, immune, unspecified

Foundation entity

Evans syndrome – http://id.who.int/icd/entity/1048228553

Part of: 3A20: Acquired haemolytic anaemia, immune › 03: Diseases of the blood or blood-forming organs