Sideroblastic anaemia

Description

Sideroblastic anaemias are a group of disorders in which haemoglobin is insufficiently synthesized, because of defective use of iron (although plasmatic iron levels may be normal or elevated). They are said to be sideroblastic because of the presence of ringed sideroblasts in the blood due to accumulated ferritin in mitochondria. Anaemias may be microcytic hypochrome (in thalassemia and hereditary sideroblastic anaemias), or macrocytic (in idiopathic acquired sideroblastic anaemias).

Exclusions from above levels

04 – Diseases of the immune system
05 – Endocrine, nutritional or metabolic diseases
18 – Complications of pregnancy, childbirth or the puerperium

Show allHide

19 – Certain conditions originating in the perinatal period
20 – Congenital malformations, deformations or chromosomal abnormalities
22 – Injury, poisoning or certain other consequences of external causes
http://id.who.int/icd/entity/1000704511 – Human immunodeficiency virus disease
JB64.1 – Other diseases of the blood or blood-forming organs or certain disorders involving the immune mechanism complicating pregnancy, childbirth or the puerperium

Child codes

3A72.0 – Congenital sideroblastic anaemias
3A72.1 – Acquired sideroblastic anaemias
3A72.Z – Sideroblastic anaemia, unspecified

Sibling codes

3A50 – Thalassaemias
3A51 – Sickle cell disorders or other haemoglobinopathies
3A70 – Aplastic anaemia
3A71 – Anaemia due to chronic disease
3A73 – Congenital dyserythropoietic anaemia
3A90 – Anaemia due to acute disease
3A91 – Congenital methaemoglobinaemia
3A92 – Hereditary methaemoglobinaemia
3A93 – Acquired methaemoglobinaemia
3A94 – Acute posthaemorrhagic anaemia
3A9Y – Other specified anaemias or erythrocyte disorders
3A9Z – Anaemias or other erythrocyte disorders, unspecified

Foundation entity

Sideroblastic anaemia – http://id.who.int/icd/entity/235504456

Part of: 03: Diseases of the blood or blood-forming organs