3B10.0

ICD-11 MMS 2026-01

Haemophilia A

Description

Haemophilia A is the most common form of haemophilia characterised by spontaneous or prolonged haemorrhages due to factor VIII deficiency. Depending on the extent of the factor VIII deficiency, it can be severe (biological activity of factor VIII below 1%), moderately severe (activity of factor VIII between 1% and 5%), or mild (activity of factor VIII between 5 and 40%).

Index terms

  • Haemophilia A
  • AHG - [antihaemophilic globulin] deficiency
  • AHG - [antihaemophilic globulin] deficiency disease
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  • Haemophilia NOS
  • antihaemophilic globulin deficiency
  • classic haemophilia
  • congenital factor VIII disorder
  • familial haemophilia
  • haemophilia
  • hereditary haemophilia
  • sex-linked factor VIII deficiency
  • subhaemophilia
  • Severe haemophilia A
  • Moderately severe haemophilia A
  • Mild haemophilia A
  • Symptomatic form of haemophilia A in female carriers

Inclusions

  • Severe haemophilia A
  • Moderately severe haemophilia A
  • Mild haemophilia A
  • Symptomatic form of haemophilia A in female carriers

Excludes

  • 3B12 – factor VIII deficiency with vascular defect

Exclusions from above levels

  • JA43.3 – Postpartum coagulation defects
  • 04 – Diseases of the immune system
  • 05 – Endocrine, nutritional or metabolic diseases
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  • 18 – Complications of pregnancy, childbirth or the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations or chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes
  • http://id.who.int/icd/entity/1000704511 – Human immunodeficiency virus disease
  • JB64.1 – Other diseases of the blood or blood-forming organs or certain disorders involving the immune mechanism complicating pregnancy, childbirth or the puerperium

Sibling codes

  • 3B10.1 – Hereditary factor VIII deficiency with anti-factor VIII inhibitor
  • 3B10.Y – Other specified hereditary factor VIII deficiency
  • 3B10.Z – Hereditary factor VIII deficiency, unspecified

Foundation entity

Haemophilia A – http://id.who.int/icd/entity/337607970

Allowed postcoordination axes

Part of: 3B10: Hereditary factor VIII deficiency › 03: Diseases of the blood or blood-forming organs