3B15

ICD-11 MMS 2026-01

Inherited coagulation factor deficiency without bleeding tendency

Description

A disease caused by a genetically inherited mutation leading to decreased levels of coagulation factor. This disease is characterised by decreased levels of coagulation factor without leading to increased haemorrhaging. Confirmation is by identification of decreased levels of coagulation factor in a blood sample.

Index terms

  • Inherited coagulation factor deficiency without bleeding tendency
  • Congenital prekallikrein deficiency
  • Congenital high-molecular-weight kininogen deficiency
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  • Hereditary factor XII deficiency
  • Congenital Hageman factor deficiency
  • Deficiency of factor XII
  • Hageman defect
  • Hageman deficiency
  • Hageman factor defect
  • Hageman factor deficiency
  • congenital factor XII deficiency
  • factor XII deficiency disease

Exclusions from above levels

  • JA43.3 – Postpartum coagulation defects
  • 04 – Diseases of the immune system
  • 05 – Endocrine, nutritional or metabolic diseases
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  • 18 – Complications of pregnancy, childbirth or the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations or chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes
  • http://id.who.int/icd/entity/1000704511 – Human immunodeficiency virus disease
  • JB64.1 – Other diseases of the blood or blood-forming organs or certain disorders involving the immune mechanism complicating pregnancy, childbirth or the puerperium

Sibling codes

  • 3B10 – Hereditary factor VIII deficiency
  • 3B11 – Hereditary factor IX deficiency
  • 3B12 – Von Willebrand disease
  • 3B13 – Haemophilia C
  • 3B14 – Other inherited coagulation factor deficiency with bleeding tendency
  • 3B1Z – Congenital or constitutional haemorrhagic condition, unspecified

Foundation entity

Inherited coagulation factor deficiency without bleeding tendency – http://id.who.int/icd/entity/1795705470

Part of: 03: Diseases of the blood or blood-forming organs