Other inherited coagulation factor deficiency with bleeding tendency

Description

Any disease caused by genetically inherited mutations leading to lack of coagulation factors in the blood not elsewhere classified. These diseases are characterised by increased haemorrhaging and bruising as the blood cannot clot properly to control bleeding. Confirmation is identification of mutations by genetic testing.

Exclusions from above levels

JA43.3 – Postpartum coagulation defects
04 – Diseases of the immune system
05 – Endocrine, nutritional or metabolic diseases

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18 – Complications of pregnancy, childbirth or the puerperium
19 – Certain conditions originating in the perinatal period
20 – Congenital malformations, deformations or chromosomal abnormalities
22 – Injury, poisoning or certain other consequences of external causes
http://id.who.int/icd/entity/1000704511 – Human immunodeficiency virus disease
JB64.1 – Other diseases of the blood or blood-forming organs or certain disorders involving the immune mechanism complicating pregnancy, childbirth or the puerperium

Child codes

3B14.0 – Hereditary deficiency of factor I
3B14.1 – Hereditary factor X deficiency
3B14.2 – Combined deficiency of vitamin K-dependent clotting factors
3B14.Z – Other inherited coagulation factor deficiency with bleeding tendency, unspecified

Sibling codes

3B10 – Hereditary factor VIII deficiency
3B11 – Hereditary factor IX deficiency
3B12 – Von Willebrand disease
3B13 – Haemophilia C
3B15 – Inherited coagulation factor deficiency without bleeding tendency
3B1Z – Congenital or constitutional haemorrhagic condition, unspecified

Foundation entity

Other inherited coagulation factor deficiency with bleeding tendency – http://id.who.int/icd/entity/573771682

Part of: 03: Diseases of the blood or blood-forming organs