3B65

ICD-11 MMS 2026-01

Thrombotic microangiopathy, not elsewhere classified

Description

Thrombotic microangiopathies are microvascular occlusive disorders characterised by systemic or intrarenal aggregation of platelets, thrombocytopenia, and mechanical injury to erythrocytes. Thrombotic thrombocytopenic purpura (TTP) and haemolytic–uremic syndrome (HUS) represent a spectrum of thrombotic microangiopathies. In TTP, systemic microvascular aggregation of platelets causes ischemia in the brain and other organs. In HUS, platelet–fibrin thrombi predominantly occlude the renal circulation.

Index terms

  • Thrombotic microangiopathy, not elsewhere classified
  • Acute intravascular thrombotic microangiopathy
  • Acute intravascular thrombi microangiopathy
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  • Chronic intravascular thrombotic microangiopathy
  • Chronic intravascular thrombi microangiopathy

Exclusions from above levels

  • JA43.3 – Postpartum coagulation defects
  • 04 – Diseases of the immune system
  • 05 – Endocrine, nutritional or metabolic diseases
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  • 18 – Complications of pregnancy, childbirth or the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations or chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes
  • http://id.who.int/icd/entity/1000704511 – Human immunodeficiency virus disease
  • JB64.1 – Other diseases of the blood or blood-forming organs or certain disorders involving the immune mechanism complicating pregnancy, childbirth or the puerperium

Foundation children elsewhere

  • 3A21.2 – Haemolytic uraemic syndrome
  • 3B64.14 – Thrombotic thrombocytopenic purpura

Sibling codes

  • 3B60 – Non-thrombocytopenic purpura
  • 3B61 – Thrombophilia
  • 3B62 – Qualitative platelet defects
  • 3B63 – Thrombocytosis
  • 3B64 – Thrombocytopenia
  • 3B6Y – Other specified coagulation defects, purpura or other haemorrhagic or related conditions
  • 3B6Z – Coagulation defects, purpura or other haemorrhagic or related conditions, unspecified

Foundation entity

Thrombotic microangiopathy, not elsewhere classified – http://id.who.int/icd/entity/757747508

Allowed postcoordination axes

Part of: 03: Diseases of the blood or blood-forming organs