4A00

ICD-11 MMS 2026-01

Primary immunodeficiencies due to disorders of innate immunity

Exclusions from above levels

  • 02 – Neoplasms
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 20 – Developmental anomalies

Child codes

  • 4A00.0 – Functional neutrophil defects
  • 4A00.1 – Defects in the complement system
  • 4A00.2 – Genetic susceptibility to particular pathogens
  • 4A00.3 – Immunodeficiency with natural-killer cell deficiency
  • 4A00.Y – Other specified primary immunodeficiencies due to disorders of innate immunity
  • 4A00.Z – Primary immunodeficiencies due to disorders of innate immunity, unspecified

Foundation children elsewhere

  • 4B00.00 – Constitutional neutropaenia

Sibling codes

  • 4A01 – Primary immunodeficiencies due to disorders of adaptive immunity
  • 4A0Y – Other specified primary immunodeficiencies
  • 4A0Z – Primary immunodeficiencies, unspecified

Foundation entity

Primary immunodeficiencies due to disorders of innate immunity – http://id.who.int/icd/entity/551037838

Part of: 04: Diseases of the immune system