4A00.0

ICD-11 MMS 2026-01

Functional neutrophil defects

Inclusions

  • Congenital dysphagocytosis

Exclusions from above levels

  • 02 – Neoplasms
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 20 – Developmental anomalies

Child codes

  • 4A00.00 – Neutrophil immunodeficiency syndrome
  • 4A00.0Y – Other specified functional neutrophil defects
  • 4A00.0Z – Functional neutrophil defects, unspecified

Foundation children elsewhere

  • 3A10.00 – Haemolytic anaemia due to glucose-6-phosphate dehydrogenase deficiency

Sibling codes

  • 4A00.1 – Defects in the complement system
  • 4A00.2 – Genetic susceptibility to particular pathogens
  • 4A00.3 – Immunodeficiency with natural-killer cell deficiency
  • 4A00.Y – Other specified primary immunodeficiencies due to disorders of innate immunity
  • 4A00.Z – Primary immunodeficiencies due to disorders of innate immunity, unspecified

Foundation entity

Functional neutrophil defects – http://id.who.int/icd/entity/808756909

Part of: 4A00: Primary immunodeficiencies due to disorders of innate immunity › 04: Diseases of the immune system