Neutrophil immunodeficiency syndrome

Description

Neutrophil immunodeficiency syndrome is a primary immunodeficiency characterised by neutrophilia with severe neutrophil dysfunction, leukocytosis, a predisposition to bacterial infections and poor wound healing, including an absence of pus in infected areas.

Index terms

Neutrophil immunodeficiency syndrome
Rac 2 deficiency

Exclusions from above levels

02 – Neoplasms
18 – Complications of pregnancy, childbirth and the puerperium
20 – Developmental anomalies

Sibling codes

4A00.0Y – Other specified functional neutrophil defects
4A00.0Z – Functional neutrophil defects, unspecified

Foundation entity

Neutrophil immunodeficiency syndrome – http://id.who.int/icd/entity/1459690929

Part of: 4A00.0: Functional neutrophil defects › 4A00: Primary immunodeficiencies due to disorders of innate immunity › 04: Diseases of the immune system