Immunodeficiency with factor D anomaly

Description

Factor D deficiency is an autosomal recessive immunologic disorder characterised by increased susceptibility to bacterial infections, particularly Neisseria infections, due to a defect in the alternative complement pathway.

Index terms

Immunodeficiency with factor D anomaly
CFDD - [Complement factor D deficiency]

Exclusions from above levels

3A10.Y – Atypical haemolytic uraemic syndrome
3A21.0 – Paroxysmal nocturnal haemoglobinuria
02 – Neoplasms

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18 – Complications of pregnancy, childbirth and the puerperium
20 – Developmental anomalies

Sibling codes

4A00.10 – Immunodeficiency with an early component of complement deficiency
4A00.11 – Immunodeficiency with a late component of complement deficiency
4A00.12 – Immunodeficiency with factor B deficiency
4A00.14 – Hereditary angioedema
4A00.15 – Acquired angioedema
4A00.1Y – Other specified defects in the complement system
4A00.1Z – Defects in the complement system, unspecified

Foundation entity

Immunodeficiency with factor D anomaly – http://id.who.int/icd/entity/1998425794

Part of: 4A00.1: Defects in the complement system › 4A00: Primary immunodeficiencies due to disorders of innate immunity › 04: Diseases of the immune system