4A01.30

ICD-11 MMS 2026-01

Immunodeficiency due to defects of the thymus

Index terms

  • Immunodeficiency due to defects of the thymus
  • Nezelof syndrome
  • Congenital thymic dysplasia syndrome
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  • Thymic aplasia
  • Immunodeficiency due to absence of thymus

Exclusions from above levels

  • 02 – Neoplasms
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 20 – Developmental anomalies

Foundation children elsewhere

Sibling codes

  • 4A01.31 – DNA repair defects other than combined T-cell or B-cell immunodeficiencies
  • 4A01.32 – Immuno-osseous dysplasia
  • 4A01.33 – Hepatic veno-occlusive disease - immunodeficiency syndrome
  • 4A01.34 – Hyperimmunoglobulin E syndromes

Foundation entity

Immunodeficiency due to defects of the thymus – http://id.who.int/icd/entity/2037626838

Part of: 4A01.3: Other well-defined immunodeficiency syndromes due to defects in adaptive immunity › 4A01: Primary immunodeficiencies due to disorders of adaptive immunity › 04: Diseases of the immune system