4A01.3

ICD-11 MMS 2026-01

Other well-defined immunodeficiency syndromes due to defects in adaptive immunity

Description

This refers to other defects in the highly specialized, systemic cells and processes that eliminate or prevent pathogen growth.

Index terms

  • Other well-defined immunodeficiency syndromes due to defects in adaptive immunity

Exclusions from above levels

  • 02 – Neoplasms
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 20 – Developmental anomalies

Child codes

  • 4A01.30 – Immunodeficiency due to defects of the thymus
  • 4A01.31 – DNA repair defects other than combined T-cell or B-cell immunodeficiencies
  • 4A01.32 – Immuno-osseous dysplasia
  • 4A01.33 – Hepatic veno-occlusive disease - immunodeficiency syndrome
  • 4A01.34 – Hyperimmunoglobulin E syndromes

Sibling codes

  • 4A01.0 – Immunodeficiencies with predominantly antibody defects
  • 4A01.1 – Combined immunodeficiencies
  • 4A01.2 – Diseases of immune dysregulation
  • 4A01.Z – Primary immunodeficiencies due to disorders of adaptive immunity, unspecified

Foundation entity

Other well-defined immunodeficiency syndromes due to defects in adaptive immunity – http://id.who.int/icd/entity/1847093418

Part of: 4A01: Primary immunodeficiencies due to disorders of adaptive immunity › 04: Diseases of the immune system