Haemophagocytic syndrome associated with infection

Description

This is an uncommon hematologic disorder that, typically, clinically manifests as fever, hepatosplenomegaly, lymphadenopathy, jaundice and rash, with laboratory findings of histiocytosis, and the pathologic finding of haemophagocytosis, infection-associated.

Index terms

Haemophagocytic syndrome associated with infection
haemophagocytic histiocytosis associated with infection
infection-induced haemophagocytic histiocytosis

Exclusions from above levels

02 – Neoplasms
18 – Complications of pregnancy, childbirth and the puerperium
20 – Developmental anomalies

Sibling codes

4A20.21 – Haemophagocytic lymphohistiocytosis associated with a malignant disease
4A20.2Y – Other specified secondary haemophagocytic lymphohistiocytosis
4A20.2Z – Secondary haemophagocytic lymphohistiocytosis, unspecified

Foundation entity

Haemophagocytic syndrome associated with infection – http://id.who.int/icd/entity/778191161

Allowed postcoordination axes

Part of: 4A20.2: Secondary haemophagocytic lymphohistiocytosis › 4A20: Acquired immunodeficiencies › 04: Diseases of the immune system