4A20.21

ICD-11 MMS 2026-01

Haemophagocytic lymphohistiocytosis associated with a malignant disease

Index terms

  • Haemophagocytic lymphohistiocytosis associated with a malignant disease
  • haemophagocytic syndrome associated with a malignancy
  • malignancy-induced haemophagocytic histiocytosis

Exclusions from above levels

  • 02 – Neoplasms
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 20 – Developmental anomalies

Sibling codes

  • 4A20.20 – Haemophagocytic syndrome associated with infection
  • 4A20.2Y – Other specified secondary haemophagocytic lymphohistiocytosis
  • 4A20.2Z – Secondary haemophagocytic lymphohistiocytosis, unspecified

Foundation entity

Haemophagocytic lymphohistiocytosis associated with a malignant disease – http://id.who.int/icd/entity/133616951

Allowed postcoordination axes

Part of: 4A20.2: Secondary haemophagocytic lymphohistiocytosis › 4A20: Acquired immunodeficiencies › 04: Diseases of the immune system