Sneddon syndrome

Description

Sneddon syndrome associates livedo reticularis and neurological signs. Livedo is permanent, cyanotic, with no infiltration, and affects the limbs, trunk and sometimes the face. Neurological signs appear later and include cerebrovascular accidents, epilepsy, vertigo and more rarely a pseudobulbar syndrome, chorea, episodes of amnesia or transient amaurosis.

Index terms

Sneddon syndrome

Exclusions from above levels

02 – Neoplasms
18 – Complications of pregnancy, childbirth and the puerperium
20 – Developmental anomalies

Sibling codes

4A44.0 – Rhizomelic pseudopolyarthritis
4A44.1 – Aortic arch syndrome
4A44.2 – Giant cell arteritis
4A44.3 – Single organ vasculitis
4A44.4 – Polyarteritis nodosa
4A44.5 – Mucocutaneous lymph node syndrome
4A44.7 – Primary angiitis of the central nervous system
4A44.8 – Thromboangiitis obliterans
4A44.9 – Immune complex small vessel vasculitis
4A44.A – Antineutrophil cytoplasmic antibody-associated vasculitis
4A44.B – Leukocytoclastic vasculitis
4A44.Y – Other specified vasculitis
4A44.Z – Vasculitis, unspecified

Foundation entity

Sneddon syndrome – http://id.who.int/icd/entity/1474816492

Part of: 4A44: Vasculitis › 04: Diseases of the immune system