4A44.9

ICD-11 MMS 2026-01

Immune complex small vessel vasculitis

Exclusions from above levels

  • 02 – Neoplasms
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 20 – Developmental anomalies

Child codes

  • 4A44.90 – Cryoglobulinaemic vasculitis
  • 4A44.91 – Hypocomplementaemic urticarial vasculitis
  • 4A44.92 – IgA vasculitis
  • 4A44.9Y – Other specified immune complex small vessel vasculitis
  • 4A44.9Z – Immune complex small vessel vasculitis, unspecified

Foundation children elsewhere

  • MF85 – Anti-glomerular basement membrane antibody mediated disease

Sibling codes

  • 4A44.0 – Rhizomelic pseudopolyarthritis
  • 4A44.1 – Aortic arch syndrome
  • 4A44.2 – Giant cell arteritis
  • 4A44.3 – Single organ vasculitis
  • 4A44.4 – Polyarteritis nodosa
  • 4A44.5 – Mucocutaneous lymph node syndrome
  • 4A44.6 – Sneddon syndrome
  • 4A44.7 – Primary angiitis of the central nervous system
  • 4A44.8 – Thromboangiitis obliterans
  • 4A44.A – Antineutrophil cytoplasmic antibody-associated vasculitis
  • 4A44.B – Leukocytoclastic vasculitis
  • 4A44.Y – Other specified vasculitis
  • 4A44.Z – Vasculitis, unspecified

Foundation entity

Immune complex small vessel vasculitis – http://id.who.int/icd/entity/548938147

Part of: 4A44: Vasculitis › 04: Diseases of the immune system