Antineutrophil cytoplasmic antibody-associated vasculitis

Description

Necrotizing vasculitis, with few or no immune deposits, predominantly affecting small vessels (i.e., capillaries, venules, arterioles and small arteries), associated with MPO-ANCA or PR3-ANCA. Not all patients have ANCA. Add a prefix indicating ANCA reactivity, e.g. PR3-ANCA, MPO-ANCA, ANCA-negative.

Exclusions from above levels

02 – Neoplasms
18 – Complications of pregnancy, childbirth and the puerperium
20 – Developmental anomalies

Child codes

4A44.A0 – Microscopic polyangiitis
4A44.A1 – Granulomatosis with polyangiitis
4A44.A2 – Eosinophilic granulomatosis with polyangiitis
4A44.AY – Other specified antineutrophil cytoplasmic antibody-associated vasculitis
4A44.AZ – Antineutrophil cytoplasmic antibody-associated vasculitis, unspecified

Sibling codes

4A44.0 – Rhizomelic pseudopolyarthritis
4A44.1 – Aortic arch syndrome
4A44.2 – Giant cell arteritis
4A44.3 – Single organ vasculitis
4A44.4 – Polyarteritis nodosa
4A44.5 – Mucocutaneous lymph node syndrome
4A44.6 – Sneddon syndrome
4A44.7 – Primary angiitis of the central nervous system
4A44.8 – Thromboangiitis obliterans
4A44.9 – Immune complex small vessel vasculitis
4A44.B – Leukocytoclastic vasculitis
4A44.Y – Other specified vasculitis
4A44.Z – Vasculitis, unspecified

Foundation entity

Antineutrophil cytoplasmic antibody-associated vasculitis – http://id.who.int/icd/entity/1404622826

Part of: 4A44: Vasculitis › 04: Diseases of the immune system