4A44.92

ICD-11 MMS 2026-01

IgA vasculitis

Description

Vasculitis, with IgA1-dominant immune deposits, affecting small vessels (predominantly capillaries, venules, or arterioles). Often involves skin and gut, and frequently causes arthritis. Glomerulonephritis indistinguishable from IgA nephropathy may occur.

Index terms

  • IgA vasculitis
  • Allergic purpura
  • Anaphylactoid purpura
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  • HSP - (Henoch-Schönlein purpura)
  • Henoch-Schönlein purpura
  • Schönlein–Henoch purpura
  • Gastric ulcer due to IgA vasculitis
  • Noninfectious colitis due to IgA vasculitis
  • Chorea due to IgA vasculitis
  • Chorea due to Henoch-Schönlein purpura
  • Chorea due to anaphylactoid purpura

Inclusions

  • Henoch-Schönlein purpura

Exclusions from above levels

  • 02 – Neoplasms
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 20 – Developmental anomalies

Sibling codes

  • 4A44.90 – Cryoglobulinaemic vasculitis
  • 4A44.91 – Hypocomplementaemic urticarial vasculitis
  • 4A44.9Y – Other specified immune complex small vessel vasculitis
  • 4A44.9Z – Immune complex small vessel vasculitis, unspecified

Foundation entity

IgA vasculitis – http://id.who.int/icd/entity/1629105375

Allowed postcoordination axes

Part of: 4A44.9: Immune complex small vessel vasculitis › 4A44: Vasculitis › 04: Diseases of the immune system