4A44.92ICD-11 MMS 2026-01
IgA vasculitis
Description
Vasculitis, with IgA1-dominant immune deposits, affecting small vessels (predominantly capillaries, venules, or arterioles). Often involves skin and gut, and frequently causes arthritis. Glomerulonephritis indistinguishable from IgA nephropathy may occur.
Index terms
- IgA vasculitis
- Allergic purpura
- Anaphylactoid purpura
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- HSP - (Henoch-Schönlein purpura)
- Henoch-Schönlein purpura
- Schönlein–Henoch purpura
- Gastric ulcer due to IgA vasculitis
- Noninfectious colitis due to IgA vasculitis
- Chorea due to IgA vasculitis
- Chorea due to Henoch-Schönlein purpura
- Chorea due to anaphylactoid purpura
Inclusions
- Henoch-Schönlein purpura
Exclusions from above levels
Sibling codes
Foundation entity
Allowed postcoordination axes
Part of: 4A44.9: Immune complex small vessel vasculitis › 4A44: Vasculitis › 04: Diseases of the immune system