5C64.0

ICD-11 MMS 2026-01

Disorders of copper metabolism

Description

Any condition caused by failure to correctly metabolize copper.

Exclusions from above levels

  • 5B57 – Vitamin D deficiency
  • 5B5K – dietary mineral deficiency
  • http://id.who.int/icd/entity/962023213 – Disorders of the parathyroids or parathyroid hormone system
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  • 3A10.Z – Hereditary haemolytic anaemia due to enzyme deficiency
  • 5A71.01 – Congenital adrenal hyperplasia
  • 5A81.1 – 5-alpha-reductase deficiency
  • LD28.01 – Marfan syndrome
  • LD28.1 – Ehlers-Danlos syndrome
  • LD2A.4 – androgen resistance syndrome
  • 18 – Pregnancy, childbirth or the puerperium
  • http://id.who.int/icd/entity/1004987305 – Transitory endocrine or metabolic disorders specific to fetus or newborn

Child codes

  • 5C64.00 – Wilson disease
  • 5C64.0Y – Other specified disorders of copper metabolism
  • 5C64.0Z – Disorders of copper metabolism, unspecified

Sibling codes

  • 5C64.1 – Disorders of iron metabolism
  • 5C64.2 – Disorders of zinc metabolism
  • 5C64.3 – Disorders of phosphorus metabolism or phosphatases
  • 5C64.4 – Disorders of magnesium metabolism
  • 5C64.5 – Disorders of calcium metabolism
  • 5C64.6 – Disorders of sodium metabolism
  • 5C64.7 – Disorders of chloride metabolism
  • 5C64.Y – Disorders of other specified mineral absorption or transport
  • 5C64.Z – Disorders of mineral absorption or transport, unspecified

Foundation entity

Disorders of copper metabolism – http://id.who.int/icd/entity/1926278296

Part of: 5C64: Disorders of mineral absorption or transport › 05: Endocrine, nutritional or metabolic diseases