5C81.0

ICD-11 MMS 2026-01

Hypoalphalipoproteinaemia

Description

A disorder characterised by low levels of high-density lipoprotein in the blood.

Index terms

  • Hypoalphalipoproteinaemia
  • Familial hypoalphalipoproteinaemia
  • familial hypolipoproteinaemia
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  • familial lipoprotein deficiency
  • Apolipoprotein A-I deficiency
  • Familial lecithin-cholesterol acyltransferase deficiency
  • Complete LCAT - [lecithin-cholesterol acyltransferase] deficiency
  • Complete lecithin-cholesterol acyltransferase deficiency
  • Familial LCAT - [lecithin-cholesterol acyltransferase] deficiency
  • phosphatidylcholine-sterol acyltransferase deficiency
  • Fish-eye disease
  • Dyslipoproteinaemic corneal dystrophy
  • Ophthalmic ichthyosis
  • Partial LCAT - [lecithin-cholesterol acyltransferase] deficiency
  • Partial lecithin-cholesterol acyltransferase deficiency
  • Norum disease
  • Analphalipoproteinaemia
  • Tangier disease
  • cholesterol thesaurismosis
  • Secondary hypoalphalipoproteinaemia

Exclusions from above levels

  • 5C56.0 – Sphingolipidosis
  • 3A10.Z – Hereditary haemolytic anaemia due to enzyme deficiency
  • 5A71.01 – Congenital adrenal hyperplasia
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  • 5A81.1 – 5-alpha-reductase deficiency
  • LD28.01 – Marfan syndrome
  • LD28.1 – Ehlers-Danlos syndrome
  • LD2A.4 – androgen resistance syndrome
  • 18 – Pregnancy, childbirth or the puerperium
  • http://id.who.int/icd/entity/1004987305 – Transitory endocrine or metabolic disorders specific to fetus or newborn

Sibling codes

  • 5C81.1 – Hypobetalipoproteinaemia
  • 5C81.Y – Other specified hypolipoproteinaemia
  • 5C81.Z – Hypolipoproteinaemia, unspecified

Foundation entity

Hypoalphalipoproteinaemia – http://id.who.int/icd/entity/1731667610

Part of: 5C81: Hypolipoproteinaemia › 05: Endocrine, nutritional or metabolic diseases