5C81

ICD-11 MMS 2026-01

Hypolipoproteinaemia

Description

Disorders characterised by low level of lipoproteins of any type in the blood

Inclusions

  • High-density lipoprotein deficiency

Exclusions from above levels

  • 5C56.0 – Sphingolipidosis
  • 3A10.Z – Hereditary haemolytic anaemia due to enzyme deficiency
  • 5A71.01 – Congenital adrenal hyperplasia
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  • 5A81.1 – 5-alpha-reductase deficiency
  • LD28.01 – Marfan syndrome
  • LD28.1 – Ehlers-Danlos syndrome
  • LD2A.4 – androgen resistance syndrome
  • 18 – Pregnancy, childbirth or the puerperium
  • http://id.who.int/icd/entity/1004987305 – Transitory endocrine or metabolic disorders specific to fetus or newborn

Child codes

  • 5C81.0 – Hypoalphalipoproteinaemia
  • 5C81.1 – Hypobetalipoproteinaemia
  • 5C81.Y – Other specified hypolipoproteinaemia
  • 5C81.Z – Hypolipoproteinaemia, unspecified

Sibling codes

  • 5C80 – Hyperlipoproteinaemia
  • 5C8Y – Other specified disorders of lipoprotein metabolism or lipidaemias
  • 5C8Z – Unspecified disorders of lipoprotein metabolism or lipidaemias

Foundation entity

Hypolipoproteinaemia – http://id.who.int/icd/entity/526909365

Part of: 05: Endocrine, nutritional or metabolic diseases