ICD-11 MMS 2026-01
Other specified metabolic disorders
Exclusions from above levels
2B31.2 – histiocytosis X (chronic)3A10.Z – Hereditary haemolytic anaemia due to enzyme deficiency5A71.01 – Congenital adrenal hyperplasia
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5A81.1 – 5-alpha-reductase deficiencyLD28.01 – Marfan syndromeLD28.1 – Ehlers-Danlos syndromeLD2A.4 – androgen resistance syndrome18 – Pregnancy, childbirth or the puerperium- http://id.who.int/icd/entity/1004987305 – Transitory endocrine or metabolic disorders specific to fetus or newborn
Sibling codes
5D00 – Amyloidosis5D01 – Tumour lysis syndrome
Allowed postcoordination axes
Part of: 05: Endocrine, nutritional or metabolic diseases