Amyloidosis

Description

Amyloidosis is a vast group of diseases defined by the presence of insoluble protein deposits in tissues. Its diagnosis is based on histological findings. Amyloidoses are classified according to clinical signs and biochemical type of amyloid protein involved. Most amyloidoses are multisystemic, 'generalised' or 'diffuse'. There are a few forms of localised amylosis. The most frequent forms are AL amyloidosis (immunoglobulins), AA (inflammatory), and ATTR (transthyretin accumulation).

Excludes

• 6D80 – Dementia due to Alzheimer disease

Exclusions from above levels

• 2B31.2 – histiocytosis X (chronic)
• 3A10.Z – Hereditary haemolytic anaemia due to enzyme deficiency
• 5A71.01 – Congenital adrenal hyperplasia