8A03.1

ICD-11 MMS 2026-01

Hereditary ataxia

Description

A group of genetic disorders characterised by slowly progressive incoordination of gait and often associated with poor coordination of hands, speech, and eye movements

Excludes

  • http://id.who.int/icd/entity/155258022 – Metabolic disorders
  • http://id.who.int/icd/entity/76906748 – Cerebral palsy

Exclusions from above levels

  • 6A06 – Stereotyped movement disorder
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
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  • 19 – Certain conditions originating in the perinatal period
  • 22 – Injury, poisoning or certain other consequences of external causes

Child codes

  • 8A03.10 – Friedreich ataxia
  • 8A03.11 – Ataxia due to Cerebrotendinous xanthomatosis
  • 8A03.12 – Ataxia due to Refsum disease
  • 8A03.13 – Ataxia due to abetalipoproteinemia
  • 8A03.14 – Hereditary episodic ataxia
  • 8A03.15 – Ataxia due to mitochondrial mutations
  • 8A03.16 – Spinocerebellar ataxia
  • 8A03.1Y – Other specified hereditary ataxia
  • 8A03.1Z – Hereditary ataxia, unspecified

Sibling codes

  • 8A03.0 – Congenital ataxia
  • 8A03.2 – Non-hereditary degenerative ataxia
  • 8A03.3 – Acquired ataxia
  • 8A03.Y – Other specified ataxic disorders
  • 8A03.Z – Ataxic disorders, unspecified

Foundation entity

Hereditary ataxia – http://id.who.int/icd/entity/442347652

Part of: 8A03: Ataxic disorders › 08: Diseases of the nervous system