8A03.16

ICD-11 MMS 2026-01

Spinocerebellar ataxia

Description

Autosomal dominantly inherited ataxias associated with over 37 gene loci that involve progressive degeneration of the cerebellum and spinocerebellar tracts of the spinal cord, presenting with characteristic sensory loss, diminished tendon reflexes, Romberg sign, and positive Babinski sign(s).

Index terms

  • Spinocerebellar ataxia
  • Autosomal dominant cerebellar ataxia type 1
  • Spinocerebellar ataxia type 1
Show allHide
  • Spinocerebellar ataxia type 12
  • Spinocerebellar ataxia type 13
  • Spinocerebellar ataxia type 16
  • Spinocerebellar ataxia type 17
  • Spinocerebellar ataxia type 18
  • Spinocerebellar ataxia type 19
  • Spinocerebellar ataxia type 2
  • Spinocerebellar ataxia type 21
  • Spinocerebellar ataxia type 22
  • Spinocerebellar ataxia type 23
  • Spinocerebellar ataxia type 27
  • Spinocerebellar ataxia type 28
  • Spinocerebellar ataxia type 3
  • Machado-Joseph disease
  • Machado-Joseph disease type 1
  • Machado-Joseph disease type 2
  • Machado-Joseph disease type 3
  • Spinocerebellar ataxia type 32
  • Spinocerebellar ataxia type 35
  • Spinocerebellar ataxia type 36
  • Spinocerebellar ataxia type 4
  • Spinocerebellar ataxia type 8
  • Autosomal dominant cerebellar ataxia type 2
  • Spinocerebellar ataxia type 7
  • Autosomal dominant cerebellar ataxia type 3
  • Spinocerebellar ataxia type 10
  • Spinocerebellar ataxia type 11
  • Spinocerebellar ataxia type 14
  • Spinocerebellar ataxia type 15
  • Spinocerebellar ataxia type 15/16
  • Spinocerebellar ataxia type 20
  • Spinocerebellar ataxia type 25
  • Spinocerebellar ataxia type 26
  • Spinocerebellar ataxia type 29
  • Spinocerebellar ataxia type 30
  • Spinocerebellar ataxia type 31
  • Spinocerebellar ataxia type 5
  • Spinocerebellar ataxia type 6
  • Autosomal dominant cerebellar ataxia type 4

Exclusions from above levels

  • http://id.who.int/icd/entity/155258022 – Metabolic disorders
  • http://id.who.int/icd/entity/76906748 – Cerebral palsy
  • 6A06 – Stereotyped movement disorder
Show allHide
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • 8A03.10 – Friedreich ataxia
  • 8A03.11 – Ataxia due to Cerebrotendinous xanthomatosis
  • 8A03.12 – Ataxia due to Refsum disease
  • 8A03.13 – Ataxia due to abetalipoproteinemia
  • 8A03.14 – Hereditary episodic ataxia
  • 8A03.15 – Ataxia due to mitochondrial mutations
  • 8A03.1Y – Other specified hereditary ataxia
  • 8A03.1Z – Hereditary ataxia, unspecified

Foundation entity

Spinocerebellar ataxia – http://id.who.int/icd/entity/600993818

Part of: 8A03.1: Hereditary ataxia › 8A03: Ataxic disorders › 08: Diseases of the nervous system