8A61.0

ICD-11 MMS 2026-01

Genetic epileptic syndromes with neonatal onset

Description

Epilepsy with onset in the first 30 days of life resulting from one or more known or presumed genetic defects in which seizures are the core symptom of the disorder.

Coding note from above levels

Use additional code, if desired, to identify the type of seizure.

Excludes

  • 8A60.0 – Epilepsy due to prenatal or perinatal brain insults
  • KB06 – Neonatal seizures

Exclusions from above levels

  • MG45 – Syncope
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
Show allHide
  • 19 – Certain conditions originating in the perinatal period
  • 22 – Injury, poisoning or certain other consequences of external causes

Child codes

  • 8A61.00 – Pyridoxal dependent epilepsy
  • 8A61.0Y – Other specified genetic epileptic syndromes with neonatal onset
  • 8A61.0Z – Genetic epileptic syndromes with neonatal onset, unspecified

Sibling codes

  • 8A61.1 – Genetic epileptic syndromes with onset in infancy
  • 8A61.2 – Genetic epileptic syndromes with childhood onset
  • 8A61.3 – Genetic epileptic syndrome with adolescent or adult onset
  • 8A61.4 – Genetic epileptic syndromes with variable age of onset
  • 8A61.Y – Other specified genetic or presumed genetic syndromes primarily expressed as epilepsy
  • 8A61.Z – Genetic or presumed genetic syndromes primarily expressed as epilepsy, unspecified

Foundation entity

Genetic epileptic syndromes with neonatal onset – http://id.who.int/icd/entity/1136270486

Allowed postcoordination axes

Part of: 8A61: Genetic or presumed genetic syndromes primarily expressed as epilepsy › 08: Diseases of the nervous system