8A61.1

ICD-11 MMS 2026-01

Genetic epileptic syndromes with onset in infancy

Description

Include a vast spectrum of phenotypes having in common a genetic background and the onset in infancy. They range from benign self-remitting to severe drug resistant syndromes. Family history of epilepsy is common in some syndromic entities and exceptional in others.

Coding note from above levels

Use additional code, if desired, to identify the type of seizure.

Exclusions from above levels

  • MG45 – Syncope
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
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  • 19 – Certain conditions originating in the perinatal period
  • 22 – Injury, poisoning or certain other consequences of external causes

Child codes

  • 8A61.10 – Benign familial infantile epilepsy
  • 8A61.11 – Dravet syndrome
  • 8A61.12 – Epilepsy of infancy with migrating focal seizures
  • 8A61.1Y – Other specified genetic epileptic syndromes with onset in infancy
  • 8A61.1Z – Genetic epileptic syndromes with onset in infancy, unspecified

Sibling codes

  • 8A61.0 – Genetic epileptic syndromes with neonatal onset
  • 8A61.2 – Genetic epileptic syndromes with childhood onset
  • 8A61.3 – Genetic epileptic syndrome with adolescent or adult onset
  • 8A61.4 – Genetic epileptic syndromes with variable age of onset
  • 8A61.Y – Other specified genetic or presumed genetic syndromes primarily expressed as epilepsy
  • 8A61.Z – Genetic or presumed genetic syndromes primarily expressed as epilepsy, unspecified

Foundation entity

Genetic epileptic syndromes with onset in infancy – http://id.who.int/icd/entity/1310497511

Allowed postcoordination axes

Part of: 8A61: Genetic or presumed genetic syndromes primarily expressed as epilepsy › 08: Diseases of the nervous system