8A61.10

ICD-11 MMS 2026-01

Benign familial infantile epilepsy

Description

Epilepsy characterised by the occurrence of repeated seizures in healthy infants with no prior medical history during the first year of life. The seizures manifest with motor arrest, impairment of consciousness, staring, eye and head deviation, and mild unilateral clonic convulsions. A family history of the same epilepsy is a constant finding. The pattern of inheritance is most probably autosomal dominant.

Coding note from above levels

Use additional code, if desired, to identify the type of seizure.

Index terms

  • Benign familial infantile epilepsy
  • Watanabe-Vigevano syndrome
  • Infantile convulsions or choreoathetosis
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  • ICCA - [Infantile convulsions and choreoathetosis] syndrome
  • Infantile convulsions and paroxysmal choreoathetosis
  • Benign infantile focal epilepsy with midline spikes and waves during sleep

Exclusions from above levels

  • MG45 – Syncope
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
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  • 19 – Certain conditions originating in the perinatal period
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • 8A61.11 – Dravet syndrome
  • 8A61.12 – Epilepsy of infancy with migrating focal seizures
  • 8A61.1Y – Other specified genetic epileptic syndromes with onset in infancy
  • 8A61.1Z – Genetic epileptic syndromes with onset in infancy, unspecified

Foundation entity

Benign familial infantile epilepsy – http://id.who.int/icd/entity/1944845279

Allowed postcoordination axes

Part of: 8A61.1: Genetic epileptic syndromes with onset in infancy › 8A61: Genetic or presumed genetic syndromes primarily expressed as epilepsy › 08: Diseases of the nervous system