8B60.3

ICD-11 MMS 2026-01

Progressive muscular atrophy

Description

In progressive muscular atrophy, lower motor neuron signs in limb and trunk muscles are present without upper motor neuron involvement. Over time, some patients may progress to develop upper motor neuron signs, of which pathological evidence is common even in patients who never displayed clinical upper motor neuron signs, suggesting that progressive muscular atrophy is a form of ALS.

Index terms

  • Progressive muscular atrophy
  • Duchenne-Aran atrophy
  • Duchenne-Aran muscle atrophy
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  • PMA - [progressive muscular atrophy]
  • hereditary SMA - [spinal muscle atrophy]
  • hereditary spinal muscle atrophy
  • progressive muscle atrophy
  • progressive spinal muscle atrophy
  • pure progressive muscular atrophy

Excludes

  • 8B60.0 – Amyotrophic lateral sclerosis
  • 8B60.Y – Fazio-Londe syndrome

Exclusions from above levels

  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
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  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • 8B60.0 – Amyotrophic lateral sclerosis
  • 8B60.1 – Progressive bulbar palsy
  • 8B60.2 – Progressive pseudobulbar palsy
  • 8B60.4 – Primary lateral sclerosis
  • 8B60.5 – Amyotrophic lateral sclerosis-Plus
  • 8B60.6 – Monomelic amyotrophy
  • 8B60.7 – Madras type motor neuron disease
  • 8B60.Y – Other specified motor neuron disease
  • 8B60.Z – Motor neuron disease, unspecified

Foundation entity

Progressive muscular atrophy – http://id.who.int/icd/entity/1282359533

Allowed postcoordination axes

Part of: 8B60: Motor neuron disease › 08: Diseases of the nervous system