8D65

ICD-11 MMS 2026-01

Cerebrospinal fluid fistula

Description

Cerebrospinal fluid fistula is a condition in which the cerebrospinal fluid (CSF) held in and around the human brain and spinal cord leaks out of the surrounding protective sac, the dura, for no apparent reason or due to several pathological processes.

Index terms

  • Cerebrospinal fluid fistula
  • Cranial cerebrospinal fluid fistula
  • Cranial cerebrospinal fluid fistula due to injuries to the head
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  • Cranial cerebrospinal fluid fistula due to tumour invasion
  • Cranial cerebrospinal fluid fistula due to shunt under-drainage
  • Spontaneous cranial cerebrospinal fluid fistula
  • Cranial cerebrospinal fluid fistula due to osteomyelitis
  • Cranial cerebrospinal fluid fistula due to empty sella
  • Cranial cerebrospinal fluid fistula due to hydrocephalus
  • Cranial cerebrospinal fluid fistula due to collagen deficiency
  • Spinal cerebrospinal fluid fistula
  • Spontaneous spinal cerebrospinal fluid fistula
  • Spinal cerebrospinal fluid fistula due to injuries to the head
  • Spinal cerebrospinal fluid fistula due to tumour invasion
  • Spinal cerebrospinal fluid fistula due to shunt under-drainage
  • Spinal cerebrospinal fluid fistula due to osteomyelitis
  • Spinal cerebrospinal fluid fistula due to collagen deficiency
  • Spinal cerebrospinal fluid fistula due to open injury to the spine

Excludes

  • 8E67 – Cerebrospinal fluid leak due to surgery or lumbar puncture

Exclusions from above levels

  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
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  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • 8D60 – Increased intracranial pressure
  • 8D61 – Intracranial hypotension
  • 8D62 – Cerebrospinal fluid rhinorrhoea
  • 8D63 – Cerebrospinal fluid otorrhoea
  • 8D64 – Hydrocephalus
  • 8D66 – Syringomyelia or syringobulbia
  • 8D67 – Intracranial arachnoid cyst
  • 8D68 – Porencephalic cyst
  • 8D6Y – Other specified disorders of cerebrospinal fluid pressure or flow
  • 8D6Z – Disorders of cerebrospinal fluid pressure or flow, unspecified

Foundation entity

Cerebrospinal fluid fistula – http://id.who.int/icd/entity/501432887

Part of: 08: Diseases of the nervous system