8D66

ICD-11 MMS 2026-01

Syringomyelia or syringobulbia

Description

In syringomyelia, there is fluid-filled tubular cavitation (syrinx formation) within the central spinal cord. The syrinx can elongate, enlarge and expand into the grey and white matter and, as it does so, it compresses the nervous tissue of the corticospinal and spinothalamic tracts and the anterior horn cells. This leads to the various neurological symptoms and signs. If the syrinx extends into the brainstem, syringobulbia results.

Excludes

  • LA07.3 – Congenital hydromyelia

Exclusions from above levels

  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
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  • 22 – Injury, poisoning or certain other consequences of external causes

Child codes

  • 8D66.0 – Idiopathic syringomyelia
  • 8D66.1 – Syringomyelia due to certain specified cause
  • 8D66.2 – Syringobulbia
  • 8D66.Y – Other specified syringomyelia or syringobulbia
  • 8D66.Z – Syringomyelia or syringobulbia, unspecified

Sibling codes

  • 8D60 – Increased intracranial pressure
  • 8D61 – Intracranial hypotension
  • 8D62 – Cerebrospinal fluid rhinorrhoea
  • 8D63 – Cerebrospinal fluid otorrhoea
  • 8D64 – Hydrocephalus
  • 8D65 – Cerebrospinal fluid fistula
  • 8D67 – Intracranial arachnoid cyst
  • 8D68 – Porencephalic cyst
  • 8D6Y – Other specified disorders of cerebrospinal fluid pressure or flow
  • 8D6Z – Disorders of cerebrospinal fluid pressure or flow, unspecified

Foundation entity

Syringomyelia or syringobulbia – http://id.who.int/icd/entity/1925186604

Allowed postcoordination axes

Part of: 08: Diseases of the nervous system