8E00

ICD-11 MMS 2026-01

Sporadic Creutzfeldt-Jakob Disease

Description

A disease of the brain, that is associated with a mutation of normal prion protein genes or spontaneous transformation of prion proteins. This disease is characterised by a long incubation period, progressive dementia, neurological deficits, and is fatal. Transmission may be by direct contact with infected nervous tissue or blood. Confirmation is by pathological examination of the brain.

Index terms

  • Sporadic Creutzfeldt-Jakob Disease
  • Creutzfeldt-Jakob disease NOS
  • idiopathic Creutzfeldt-Jakob disease
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  • sCJD - [Sporadic Creutzfeldt-Jakob Disease]
  • Classical sporadic Creutzfeldt-Jakob Disease
  • Thalamic sporadic Creutzfeldt-Jakob Disease
  • Cortical sporadic Creutzfeldt-Jakob Disease

Exclusions from above levels

  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
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  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • 8E01 – Acquired prion disease
  • 8E02 – Genetic prion diseases
  • 8E03 – Variably protease sensitive prionopathy
  • 8E0Y – Other specified human prion diseases
  • 8E0Z – Human prion diseases, unspecified

Foundation entity

Sporadic Creutzfeldt-Jakob Disease – http://id.who.int/icd/entity/1553463690

Allowed postcoordination axes

Part of: 08: Diseases of the nervous system