8E01

ICD-11 MMS 2026-01

Acquired prion disease

Description

Environmentally acquired prion diseases are prion diseases caused by a known source of abnormal prion protein.

Exclusions from above levels

  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
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  • 22 – Injury, poisoning or certain other consequences of external causes

Child codes

  • 8E01.0 – Iatrogenically acquired Creutzfeldt-Jakob Disease
  • 8E01.1 – Kuru
  • 8E01.2 – Variant Creutzfeldt-Jakob Disease
  • 8E01.3 – Other acquired Creutzfeldt-Jakob Disease
  • 8E01.Z – Acquired prion disease, unspecified

Sibling codes

  • 8E00 – Sporadic Creutzfeldt-Jakob Disease
  • 8E02 – Genetic prion diseases
  • 8E03 – Variably protease sensitive prionopathy
  • 8E0Y – Other specified human prion diseases
  • 8E0Z – Human prion diseases, unspecified

Foundation entity

Acquired prion disease – http://id.who.int/icd/entity/672974943

Allowed postcoordination axes

Part of: 08: Diseases of the nervous system