8E01.2

ICD-11 MMS 2026-01

Variant Creutzfeldt-Jakob Disease

Description

A disease of the brain, that is suspected to be caused by a prion associated with Bovine Spongiform Encephalopathy. This disease is characterised by a long incubation period, psychiatric symptoms followed by neurological deficits, and is fatal. Transmission may be by ingestion of food (with a bovine origin) contaminated with infected brain or spinal cord from an infected cow, or blood transfusion. Confirmation is by pathological examination of the brain.

Index terms

  • Variant Creutzfeldt-Jakob Disease
  • vCJD - [Variant Creutzfeldt-Jakob Disease]

Exclusions from above levels

  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
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  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • 8E01.0 – Iatrogenically acquired Creutzfeldt-Jakob Disease
  • 8E01.1 – Kuru
  • 8E01.3 – Other acquired Creutzfeldt-Jakob Disease
  • 8E01.Z – Acquired prion disease, unspecified

Foundation entity

Variant Creutzfeldt-Jakob Disease – http://id.who.int/icd/entity/378572696

Allowed postcoordination axes

Part of: 8E01: Acquired prion disease › 08: Diseases of the nervous system