9A10.1

ICD-11 MMS 2026-01

Orbital inflammatory syndrome

Description

This refers to a marginated mass-like enhancing soft tissue involving any area of the orbit. It is the most common painful orbital mass in the adult population, and is associated with proptosis, cranial nerve palsy (Tolosa-Hunt syndrome), uveitis, and retinal detachment.

Index terms

  • Orbital inflammatory syndrome

Exclusions from above levels

  • LA14.1 – congenital malformations of lacrimal system
  • 01 – Certain infectious or parasitic diseases
  • 05 – Endocrine, nutritional or metabolic diseases
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  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 22 – Injury, poisoning or certain other consequences of external causes
  • 8A21.0 – Posterior cortical atrophy

Sibling codes

  • 9A10.0 – Infections of the lacrimal gland
  • 9A10.2 – Benign lymphoepithelial lesion of lacrimal gland
  • 9A10.3 – Hyperlacrimation
  • 9A10.4 – Underproduction of tears
  • 9A10.Y – Other specified disorders of lacrimal gland
  • 9A10.Z – Disorders of lacrimal gland, unspecified

Foundation entity

Orbital inflammatory syndrome – http://id.who.int/icd/entity/1446936878

Allowed postcoordination axes

Part of: 9A10: Disorders of lacrimal gland › 09: Diseases of the visual system