Hereditary corneal dystrophies

Description

The term corneal dystrophy embraces a heterogeneous group of bilateral genetically determined non-inflammatory corneal diseases that are usually restricted to the cornea. The designation is imprecise but remains in vogue because of its clinical value.

Exclusions from above levels

01 – Certain infectious or parasitic diseases
05 – Endocrine, nutritional or metabolic diseases
18 – Complications of pregnancy, childbirth and the puerperium

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19 – Certain conditions originating in the perinatal period
22 – Injury, poisoning or certain other consequences of external causes
8A21.0 – Posterior cortical atrophy

Child codes

9A70.0 – Endothelial corneal dystrophy
9A70.Y – Other specified hereditary corneal dystrophies
9A70.Z – Hereditary corneal dystrophies, unspecified

Foundation children elsewhere

EC20.01 – X-linked ichthyosis

Sibling codes

9A71 – Infectious keratitis
9A72 – Traumatic keratitis
9A73 – Exposure keratitis
9A74 – Neurotrophic keratitis
9A75 – Autoimmune keratitis
9A76 – Corneal ulcer
9A77 – Corneal scars or opacities
9A78 – Certain specified disorders of cornea
9A79 – Keratoconjunctivitis sicca
9A7A – Corneal abscess
9A7B – Sclerosing keratitis
9A7Y – Other specified disorders of the cornea
9A7Z – Disorders of the cornea, unspecified

Foundation entity

Hereditary corneal dystrophies – http://id.who.int/icd/entity/1291475891

Allowed postcoordination axes

Part of: 09: Diseases of the visual system