9C61.40

ICD-11 MMS 2026-01

Primary congenital glaucoma

Description

Primary Congenital Glaucoma is a condition during early infancy where delayed development and malformation of the trabecular meshwork blocks the outflow routes leading to elevated intraocular pressure that causes enlargement of the eyeball (Buphthalmus), corneal oedema, Descemet tears, myopia, and damage to the optic nerve, often resulting in severe visual impairment or blindness

Index terms

  • Primary congenital glaucoma
  • Primary congenital glaucoma, unilateral
  • Primary congenital glaucoma, bilateral

Exclusions from above levels

  • KA41 – Traumatic glaucoma due to birth injury
  • 01 – Certain infectious or parasitic diseases
  • 05 – Endocrine, nutritional or metabolic diseases
Show allHide
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 22 – Injury, poisoning or certain other consequences of external causes
  • 8A21.0 – Posterior cortical atrophy

Sibling codes

  • 9C61.41 – Primary infantile glaucoma
  • 9C61.42 – Secondary childhood glaucoma
  • 9C61.4Y – Other specified developmental glaucoma
  • 9C61.4Z – Developmental glaucoma, unspecified

Foundation entity

Primary congenital glaucoma – http://id.who.int/icd/entity/517092878

Allowed postcoordination axes

Part of: 9C61.4: Developmental glaucoma › 9C61: Glaucoma › 09: Diseases of the visual system