AB31.3

ICD-11 MMS 2026-01

Superior canal dehiscence syndrome

Description

Superior canal dehiscence syndrome (SCDS) occurs when thin or dehiscent bone over the superior semicircular canal, best demonstrated on CT, allows pressure transmission between the canal and the intracranial space. Vertigo and nystagmus may occur when the canal is stimulated by loud sounds or changes in middle ear or intracranial pressure. Hyperacusis to bone-conducted sounds can cause conductive hearing loss, pulsatile tinnitus, or autophony (hearing one’s own body sounds as loud or distorted). While the bony defect may be congenital, head trauma can be the final step that opens a functionally mobile labyrinthine window.

Index terms

  • Superior canal dehiscence syndrome

Exclusions from above levels

  • 01 – Certain infectious or parasitic diseases
  • 02 – Neoplasms
  • 05 – Endocrine, nutritional or metabolic diseases
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  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • AB31.0 – Meniere disease
  • AB31.1 – Vestibular migraine
  • AB31.2 – Benign positional paroxysmal vertigo
  • AB31.4 – Disembarkment syndrome
  • AB31.5 – Autoimmune inner ear disease
  • AB31.6 – Vestibular paroxysmia
  • AB31.7 – Vertiginous syndromes
  • AB31.Y – Other specified episodic vestibular syndrome
  • AB31.Z – Episodic vestibular syndrome, unspecified

Foundation entity

Superior canal dehiscence syndrome – http://id.who.int/icd/entity/144677326

Allowed postcoordination axes

Part of: AB31: Episodic vestibular syndrome › 10: Diseases of the ear or mastoid process