Autoimmune inner ear disease

Description

Autoimmune inner ear disease (AIED) is a clinical syndrome of bilateral sensorineural hearing loss (SNHL) >30dB at one or more frequencies progressing over a period of 3-90 days. Progression of SNLH >15dB at one frequency or >10dB in two frequencies in at least one ear should be demonstrated. Vestibular symptoms may be present in 50% of patients and systemic autoimmune disease (SAD) coexists in 30% of patients.

Index terms

Autoimmune inner ear disease

Exclusions from above levels

01 – Certain infectious or parasitic diseases
02 – Neoplasms
05 – Endocrine, nutritional or metabolic diseases

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18 – Complications of pregnancy, childbirth and the puerperium
19 – Certain conditions originating in the perinatal period
22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

AB31.0 – Meniere disease
AB31.1 – Vestibular migraine
AB31.2 – Benign positional paroxysmal vertigo
AB31.3 – Superior canal dehiscence syndrome
AB31.4 – Disembarkment syndrome
AB31.6 – Vestibular paroxysmia
AB31.7 – Vertiginous syndromes
AB31.Y – Other specified episodic vestibular syndrome
AB31.Z – Episodic vestibular syndrome, unspecified

Foundation entity

Autoimmune inner ear disease – http://id.who.int/icd/entity/1392879169

Allowed postcoordination axes

Part of: AB31: Episodic vestibular syndrome › 10: Diseases of the ear or mastoid process