AB50ICD-11 MMS 2026-01
Congenital hearing impairment
Description
Both dominant and recessive genes exist which can cause mild to profound impairment. If a family has a dominant gene for deafness it will persist across generations because it will manifest itself in the offspring even if it is inherited from only one parent. If a family had genetic hearing impairment caused by a recessive gene it will not always be apparent as it will have to be passed onto offspring from both parents. Hearing impairment is sustained before the acquisition of language, which occurs due to a congenital condition.
Exclusions from above levels
Child codes
Sibling codes
AB51– Acquired hearing impairmentAB52– Deafness not otherwise specifiedAB53– Ototoxic hearing lossAB54– PresbycusisAB55– Sudden idiopathic hearing lossAB56– Hereditary hearing lossAB57– Auditory synaptopathy or neuropathyAB5Y– Other specified disorders with hearing impairmentAB5Z– Disorders with hearing impairment, unspecified
Foundation entity
Congenital hearing impairment – http://id.who.int/icd/entity/1154032108
Allowed postcoordination axes
Part of: 10: Diseases of the ear or mastoid process