AB50

ICD-11 MMS 2026-01

Congenital hearing impairment

Description

Both dominant and recessive genes exist which can cause mild to profound impairment. If a family has a dominant gene for deafness it will persist across generations because it will manifest itself in the offspring even if it is inherited from only one parent. If a family had genetic hearing impairment caused by a recessive gene it will not always be apparent as it will have to be passed onto offspring from both parents. Hearing impairment is sustained before the acquisition of language, which occurs due to a congenital condition.

Exclusions from above levels

  • AB33 – Otosclerosis
  • 01 – Certain infectious or parasitic diseases
  • 02 – Neoplasms
Show allHide
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 22 – Injury, poisoning or certain other consequences of external causes

Child codes

  • AB50.0 – Congenital conductive hearing loss
  • AB50.1 – Congenital sensorineural hearing loss
  • AB50.2 – Congenital mixed conductive and sensorineural hearing loss
  • AB50.Y – Other specified congenital hearing impairment
  • AB50.Z – Congenital hearing impairment, unspecified

Sibling codes

  • AB51 – Acquired hearing impairment
  • AB52 – Deafness not otherwise specified
  • AB53 – Ototoxic hearing loss
  • AB54 – Presbycusis
  • AB55 – Sudden idiopathic hearing loss
  • AB56 – Hereditary hearing loss
  • AB57 – Auditory synaptopathy or neuropathy
  • AB5Y – Other specified disorders with hearing impairment
  • AB5Z – Disorders with hearing impairment, unspecified

Foundation entity

Congenital hearing impairment – http://id.who.int/icd/entity/1154032108

Allowed postcoordination axes

Part of: 10: Diseases of the ear or mastoid process