BD42

ICD-11 MMS 2026-01

Raynaud phenomenon

Description

Raynaud phenomenon describes an exaggerated vascular response to cold temperature or emotional stimuli resulting in episodic digital ischaemia. It is characterised by paroxysmal vasoconstriction producing initially pallor, an essential component for the diagnosis, followed by cyanosis and erythema. Primary Raynaud disease is an isolated innocuous disorder. Secondary Raynaud phenomenon occurs in association with a wide range of different disorders including dysproteinaemias and non-organ-specific systemic autoimmune diseases.

Exclusions from above levels

  • http://id.who.int/icd/entity/1059873720 – Diseases of coronary artery
  • 01 – Certain infectious or parasitic diseases
  • 05 – Endocrine, nutritional or metabolic diseases
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  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations and chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes

Child codes

  • BD42.0 – Primary Raynaud disease
  • BD42.1 – Secondary Raynaud phenomenon
  • BD42.Z – Raynaud phenomenon, unspecified

Sibling codes

  • BD40 – Atherosclerotic chronic arterial occlusive disease
  • BD41 – Non-atherosclerotic chronic arterial occlusive disease
  • BD4Y – Other specified chronic arterial occlusive disease
  • BD4Z – Chronic arterial occlusive disease, unspecified

Foundation entity

Raynaud phenomenon – http://id.who.int/icd/entity/2038606821

Part of: 11: Diseases of the circulatory system