BD42.0ICD-11 MMS 2026-01
Primary Raynaud disease
Description
Raynaud phenomenon unassociated with any concomitant disease, drug or other provoking trauma. Criteria for diagnosis include: bilateral symmetrical episodic attacks without evidence of peripheral vascular disease or tissue injury, normal nail fold capillaroscopy, negative antinuclear antibody and normal erythrocyte sedimentation rate.
Index terms
- Primary Raynaud disease
- Raynaud disease
Inclusions
- Raynaud disease
Exclusions from above levels
Sibling codes
Foundation entity
Primary Raynaud disease – http://id.who.int/icd/entity/1592720372
Part of: BD42: Raynaud phenomenon › 11: Diseases of the circulatory system