BD42.0

ICD-11 MMS 2026-01

Primary Raynaud disease

Description

Raynaud phenomenon unassociated with any concomitant disease, drug or other provoking trauma. Criteria for diagnosis include: bilateral symmetrical episodic attacks without evidence of peripheral vascular disease or tissue injury, normal nail fold capillaroscopy, negative antinuclear antibody and normal erythrocyte sedimentation rate.

Index terms

  • Primary Raynaud disease
  • Raynaud disease

Inclusions

  • Raynaud disease

Exclusions from above levels

  • http://id.who.int/icd/entity/1059873720 – Diseases of coronary artery
  • 01 – Certain infectious or parasitic diseases
  • 05 – Endocrine, nutritional or metabolic diseases
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  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations and chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • BD42.1 – Secondary Raynaud phenomenon
  • BD42.Z – Raynaud phenomenon, unspecified

Foundation entity

Primary Raynaud disease – http://id.who.int/icd/entity/1592720372

Part of: BD42: Raynaud phenomenon › 11: Diseases of the circulatory system