BD52.0

ICD-11 MMS 2026-01

Segmental arterial mediolysis

Description

Segmental arterial mediolysis is a rare noninflammatory vascular disease of the abdominal splanchnic arteries, characterised by disruption of the arterial medial layer. It will induce multiple aneurysms in mesenteric arteries with susceptibility to vessel dissection, haemorrhage and mesenteric ischemia.

Index terms

  • Segmental arterial mediolysis

Exclusions from above levels

  • 4A44.B – Hypersensitivity angiitis
  • BD30 – Acute arterial occlusion
  • http://id.who.int/icd/entity/1008515027 – collagen (vascular) diseases
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  • http://id.who.int/icd/entity/1821859817 – Chronic arterial occlusive disease
  • http://id.who.int/icd/entity/1059873720 – Diseases of coronary artery
  • 01 – Certain infectious or parasitic diseases
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations and chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • BD52.1 – Arteriovenous fistula, acquired
  • BD52.2 – Stricture of artery
  • BD52.3 – Rupture of artery
  • BD52.4 – Necrosis of artery
  • BD52.5 – Coeliac artery compression syndrome
  • BD52.6 – Congenital great vessel related acquired abnormality
  • BD52.7 – Certain acquired abnormalities of aorta

Foundation entity

Segmental arterial mediolysis – http://id.who.int/icd/entity/1160127418

Allowed postcoordination axes

Part of: BD52: Certain specified disorders of arteries or arterioles › 11: Diseases of the circulatory system