BD52.6

ICD-11 MMS 2026-01

Congenital great vessel related acquired abnormality

Description

Any postnatal pathological change in form or function of the heart and/or great vessels consequent to the presence of congenital cardiovascular disease.

Index terms

  • Congenital great vessel related acquired abnormality
  • Acquired abnormality of common arterial trunk
  • Acquired abnormality of truncus arteriosus
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  • Acquired aneurysm of common arterial trunk
  • Acquired stenosis of common arterial trunk
  • Acquired arterial duct abnormality
  • Acquired ductus arteriosus abnormality
  • Endarteritis at site of arterial duct
  • Ascending aortopathy associated with bicuspid aortic valve
  • Ascending aortopathy associated with conotruncal malformations
  • Acquired supravalvar aortic stenosis
  • Ruptured aortic sinus of Valsalva aneurysm
  • Endarteritis at site of aortic coarctation

Excludes

  • BB02.3 – Acquired pulmonary arterial tree abnormality
  • BB03 – Acquired pulmonary venous abnormality
  • BD73 – Acquired systemic vein abnormality

Exclusions from above levels

  • 4A44.B – Hypersensitivity angiitis
  • BD30 – Acute arterial occlusion
  • http://id.who.int/icd/entity/1008515027 – collagen (vascular) diseases
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  • http://id.who.int/icd/entity/1821859817 – Chronic arterial occlusive disease
  • http://id.who.int/icd/entity/1059873720 – Diseases of coronary artery
  • 01 – Certain infectious or parasitic diseases
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations and chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes

Foundation children elsewhere

  • BC02 – Acquired abnormality of congenitally malformed valve
  • BE14.A – Postprocedural arterial duct disorder

Sibling codes

  • BD52.0 – Segmental arterial mediolysis
  • BD52.1 – Arteriovenous fistula, acquired
  • BD52.2 – Stricture of artery
  • BD52.3 – Rupture of artery
  • BD52.4 – Necrosis of artery
  • BD52.5 – Coeliac artery compression syndrome
  • BD52.7 – Certain acquired abnormalities of aorta

Foundation entity

Congenital great vessel related acquired abnormality – http://id.who.int/icd/entity/330711530

Allowed postcoordination axes

Part of: BD52: Certain specified disorders of arteries or arterioles › 11: Diseases of the circulatory system