CB04.30

ICD-11 MMS 2026-01

Idiopathic pulmonary haemosiderosis

Description

Idiopathic pulmonary hemosiderosis is a respiratory disease due to repeated episodes of diffuse alveolar haemorrhage without any underlying apparent cause, most often in children. Anaemia, cough, and pulmonary infiltrates on chest radiographs are found in majority of the patients.

Index terms

  • Idiopathic pulmonary haemosiderosis

Exclusions from above levels

  • 01 – Certain infectious or parasitic diseases
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
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  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations and chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • CB04.31 – Pulmonary alveolar proteinosis
  • CB04.3Y – Other specified alveolar or peri-alveolar conditions
  • CB04.3Z – Alveolar or peri-alveolar conditions, unspecified

Foundation entity

Idiopathic pulmonary haemosiderosis – http://id.who.int/icd/entity/1542272036

Allowed postcoordination axes

Part of: CB04.3: Alveolar or peri-alveolar conditions › CB04: Primary interstitial lung diseases specific to infancy or childhood › 12: Diseases of the respiratory system