CB04

ICD-11 MMS 2026-01

Primary interstitial lung diseases specific to infancy or childhood

Exclusions from above levels

  • 01 – Certain infectious or parasitic diseases
  • 05 – Endocrine, nutritional or metabolic diseases
  • 18 – Complications of pregnancy, childbirth and the puerperium
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  • 19 – Certain conditions originating in the perinatal period
  • 20 – Congenital malformations, deformations and chromosomal abnormalities
  • 22 – Injury, poisoning or certain other consequences of external causes

Child codes

  • CB04.0 – Diffuse pulmonary developmental disorders
  • CB04.1 – Pulmonary lymphatic dysplasia syndromes
  • CB04.2 – Disorders of surfactant metabolism
  • CB04.3 – Alveolar or peri-alveolar conditions
  • CB04.4 – Pulmonary capillaritis
  • CB04.5 – Brain-lung-thyroid syndrome
  • CB04.6 – Chronic pneumonitis of infancy
  • CB04.7 – Neuroendocrine cell hyperplasia of infancy
  • CB04.Y – Other specified primary interstitial lung diseases specific to infancy or childhood
  • CB04.Z – Primary interstitial lung diseases specific to infancy or childhood, unspecified

Sibling codes

  • CB00 – Acute respiratory distress syndrome
  • CB01 – Pulmonary oedema
  • CB02 – Pulmonary eosinophilia
  • CB03 – Idiopathic interstitial pneumonitis
  • CB05 – Interstitial lung diseases associated with systemic diseases
  • CB06 – Pulmonary alveolar microlithiasis
  • CB07 – Lymphangioleiomyomatosis
  • CB0Y – Other specified respiratory diseases principally affecting the lung interstitium
  • CB0Z – Respiratory diseases principally affecting the lung interstitium, unspecified

Foundation entity

Primary interstitial lung diseases specific to infancy or childhood – http://id.who.int/icd/entity/1408868257

Allowed postcoordination axes

Part of: 12: Diseases of the respiratory system