DB99.4

ICD-11 MMS 2026-01

Hepatopulmonary syndrome

Description

This is a syndrome of shortness of breath and hypoxemia (low oxygen levels in the blood of the arteries) caused by vasodilation (broadening of the blood vessels) in the lungs of patients with liver disease.

Index terms

  • Hepatopulmonary syndrome

Exclusions from above levels

  • 5D00.0 – amyloid degeneration of liver
  • BD71.Y – hepatic vein thrombosis
  • DB94 – alcoholic liver disease
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  • DB95 – toxic liver disease
  • DB98.3 – portal vein thrombosis
  • LB20.00 – cystic disease of liver (congenital)
  • ME10.00 – hepatomegaly NOS
  • ME10.1 – Unspecified jaundice
  • 01 – Certain infectious or parasitic diseases
  • 02 – Neoplasms
  • 05 – Endocrine, nutritional or metabolic diseases
  • 06 – Mental, behavioural or neurodevelopmental disorders
  • 18 – Complications of pregnancy, childbirth and the puerperium
  • 22 – Injury, poisoning or certain other consequences of external causes

Sibling codes

  • DB99.0 – Chronic liver disease
  • DB99.1 – Hepatic cyst
  • DB99.2 – Hepatorenal syndrome
  • DB99.3 – Portopulmonary hypertension
  • DB99.5 – Hepatic encephalopathy
  • DB99.6 – Intrahepatic cholestasis, not elsewhere classified
  • DB99.7 – Hepatic failure without mention whether acute or chronic
  • DB99.8 – Chronic hepatic failure
  • DB99.Y – Other specified diseases of liver

Foundation entity

Hepatopulmonary syndrome – http://id.who.int/icd/entity/866605228

Allowed postcoordination axes

Part of: DB99: Certain specified diseases of liver › 13: Diseases of the digestive system