EC20.0

ICD-11 MMS 2026-01

Non-syndromic ichthyosis

Description

Hereditary ichthyoses with clinical manifestations limited to the integument.

Index terms

  • Non-syndromic ichthyosis

Child codes

  • EC20.00 – Ichthyosis vulgaris
  • EC20.01 – X-linked ichthyosis
  • EC20.02 – Autosomal recessive congenital ichthyosis
  • EC20.03 – Keratinopathic ichthyoses
  • EC20.0Y – Other specified or unclassifiable non-syndromic ichthyosis

Sibling codes

  • EC20.1 – Hereditary skin peeling
  • EC20.2 – Hereditary acantholytic dermatoses
  • EC20.3 – Hereditary palmoplantar keratodermas
  • EC20.Y – Other specified genetic disorders of keratinisation

Foundation entity

Non-syndromic ichthyosis – http://id.who.int/icd/entity/213831678

Part of: EC20: Genetic disorders of keratinisation › 14: Diseases of the skin