ICD-11 MMS 2026-01
Non-syndromic ichthyosis
Description
Hereditary ichthyoses with clinical manifestations limited to the integument.
Child codes
EC20.00 – Ichthyosis vulgarisEC20.01 – X-linked ichthyosisEC20.02 – Autosomal recessive congenital ichthyosisEC20.03 – Keratinopathic ichthyosesEC20.0Y – Other specified or unclassifiable non-syndromic ichthyosis
Sibling codes
EC20.1 – Hereditary skin peelingEC20.2 – Hereditary acantholytic dermatosesEC20.3 – Hereditary palmoplantar keratodermasEC20.Y – Other specified genetic disorders of keratinisation
Part of: EC20: Genetic disorders of keratinisation › 14: Diseases of the skin