EC20.03

ICD-11 MMS 2026-01

Keratinopathic ichthyoses

Description

Heritable ichthyoses resulting from mutations in keratin genes.

Index terms

  • Keratinopathic ichthyoses
  • Epidermolytic ichthyosis
  • Bullous congenital ichthyosiform erythroderma of Brocq
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  • Congenital bullous ichthyosiform erythroderma
  • Epidermolytic hyperkeratosis
  • Superficial epidermolytic ichthyosis
  • Ichthyosis bullosa of Siemens
  • Annular epidermolytic ichthyosis
  • Autosomal recessive epidermolytic ichthyosis
  • Autosomal recessive epidermolytic hyperkeratosis
  • Naevoid epidermolytic ichthyosis
  • Ichthyosis Curth-Macklin
  • Ichthyosis hystrix, Curth-Macklin type

Sibling codes

  • EC20.00 – Ichthyosis vulgaris
  • EC20.01 – X-linked ichthyosis
  • EC20.02 – Autosomal recessive congenital ichthyosis
  • EC20.0Y – Other specified or unclassifiable non-syndromic ichthyosis

Foundation entity

Keratinopathic ichthyoses – http://id.who.int/icd/entity/992865924

Part of: EC20.0: Non-syndromic ichthyosis › EC20: Genetic disorders of keratinisation › 14: Diseases of the skin